Assessment of telescoping nail in the management of long bones fractures and deformities in patients with osteogenesis imperfecta

Background: Osteogenesis imperfecta (OI) is a genetic disorder characterized by increased bone fragility and multiple fractures. Approximately 90% are caused mutation in COL1A1 or COL1A2 genes, the disease transmitted either autosomal dominantly recessively appears as spontaneous mutation. Protein product of these two genes type I collagen, major structural protein skin, which affected quality, quantity both. The most distinct feature this repeated fractures deformities very challenging to treat. Making harder bisphosphonate treatment Intramedullary splinting long bones standard care pediatric orthopedic centers. problem treating young child with fixed length intramedullary rod, overgrowth beyond edge nail, creating segment unsupported liable deformities. need for device that elongates growth (telescoping nail) was necessary overcome problem. There were different types telescoping nails (baily-dubow, Sheffield, interlocking nail has been used imperfecta.